SciELO - Scientific Electronic Library Online

 
vol.12 número5Doenças inflamatórias alérgicas das vias aéreas superiores e suas implicações na asma brônquica: A propósito de um caso clínicoRecomendações para diagnóstico e tratamento da tuberculose latente e activa nas doenças inflamatórias articulares candidatas a tratamento com fármacos inibidores do factor de necrose tumoral alfa índice de autoresíndice de assuntosPesquisa de artigos
Home Pagelista alfabética de periódicos  

Serviços Personalizados

Journal

Artigo

Indicadores

Links relacionados

  • Não possue artigos similaresSimilares em SciELO

Compartilhar


Revista Portuguesa de Pneumologia

versão impressa ISSN 0873-2159

Rev Port Pneumol v.12 n.5 Lisboa set. 2006

 

Pneumonias intersticiais idiopáticas  – Uma revisão da literatura

 

Interstitial idiopathic pneumonias – A literature review

 

 

Paulo José de Lima Mota 1

 

 

Resumo

As pneumonias intersticiais idiopáticas (PII) são um grupo de doenças de difícil estudo e bordagem clínica, devido a vários factores, dos quais se destacam a sua raridade e a enorme discrepância nas escrições dos achados clínicos, imagiológicos e histológicos pelos vários autores. Um dos espelhos desta discrepância é o problema da classificação das várias entidades que constituem este grupo e que apenas em 2002 começou a esboçar algum consenso entre as autoridades na matéria. O objectivo desta revisão é compilar a literatura mais relevante, de modo a facilitar a compreensão de um tema tão complexo.

Palavras-chave: Pneumonias intersticiais idiopáticas, fibrose pulmonar idiopática.

 

Abstract

Interstitial idiopathic pneumonias are a group of diseases whose rarity and variety of clinical, radiological and pathological descriptions creates difficulties in study and management. An example of this is the classification method for this group, with only 2002 seeing some consensus.

The aim of this article is to review the main literature to contribute to an understanding of this subject.

Key-words: Interstitial idiopathic pneumonias, idiopathic pulmonary fibrosis.

 

 

Texto completo disponível apenas em PDF.

Full text only available in PDF format.

 

 

Bibliografia

1. Thomeer MJ et al. Comparison of registries of interstitial lung diseases in three European countries. Eur Respir J 2001; 18 (Suppl 32): 114s-8s.        [ Links ]

2. Ryu JH et al. Idiopathic Pulmonary Fibrosis: Current Concepts. Mayo Clin Proc 1998; 73:1085-01.

3. Gross TJ, Hunninghake GW. Idiopathic Pulmonary Fibrosis. N Engl J Med 2001; 345(7):517-25.

4. American Thoracic Society/European Respiratory Society International Multidisciplinary Consensus Classification of the Idiopathic Interstitial Pneumonias. Am J Respir Crit Care Med 2002; 165:277-304.

5. Harasawa M, Fukuchi Y, Morinari H. Interstitial pneumonia of unknown etiology. Tokyo: University of Tokyo Press: 1989.

6. Crystal RG, Gadek J, Ferrans V. Interstitial lung diseases: current concept of pathogenesis, staging and therapy. Am J Med 1981; 70:542-68.

7. Hamman L, Rich AR. Acute diffuse interstitial fibrosis of the lungs. Bull Johns Hopkins Hosp 1944; 74:177-212.

8. Olson J, Colby TV, Elliott CG. Hamman-Rich syndrome revisited. Mayo Clin Proc 1990; 65:1538-48.

9. Scadding JG, Hinson KF. Diffuse fibrosing alveolitis (diffuse interstitial fibrosis of the lungs): correlation of histology at biopsy with prognosis. Thorax 1967; 22:291-304.

10. Katzenstein AA, Fiorelli RF. Nonspecific Interstitial Pneumonia/Fibrosis – Histologic Features and Clinical Significance. Am J Surg Pathol 1994; 18(2):136-47.

11. Du Bois RM, Wells AU. Cryptogenic fibrosing alveolitis/idiopathic pulmonary fibrosis. Eur Respir J 2001; 18 (Suppl 32):43s-55s.

12. Carrington CB et al. Natural history and treated course of usual and desquamative interstitial pneumonia. N Engl J Med 1978; 298:801-9.

13. Davison AG et al. Cryptogenic organizing pneumonitis.  Q J Med 1983; 207:382-94.

14. Myers JL et al. Respiratory bronchiolitis causing interstitial lung disease. A clinicopathologic study of six cases. Am Rev Respir Dis 1987; 135:880-4.

15. Katzenstein AL, Myers JL. Idiopathic Pulmonary Fibrosis, clinical relevance of pathological classification. Am J Respir Crit Care Med 1998; 157:1301-15.

16. Epler GR et al. Bronchiolitis obliterans organizing pneumonia. N Engl J Med 1985; 312:152-8.

17. Cordier JF. Cryptogenic organizing pneumonitis. Clin Chest Med 1993; 14:677-92.

18. Idiopathic Pulmonary Fibrosis: Diagnosis and Treatment – International Consensus Statement. Am J Respir Crit Care Med 2000, 161:646-64.

19. Verleden GM et al. Genetic predisposition and pathogenetic mechanisms of interstitial lung diseases of unknown origin. Eur Respir J 2001, 18 (Suppl 32):17S-29S.

20. Demedts M et al. Interstitial lung diseases: an epidemiological overview. Eur Respir J 2001, 18 (Suppl 32):2S-16S.

21. King TE et al. Idiopathic pulmonary fibrosis: diagnosis and treatment. Am J Respir Crit Care Med 2000; 161:646-64.

22. Daniil ZD et al. A histologic pattern of nonspecific interstitial pneumonia is associated with a better prognosis than usual interstitial pneumonia with cryptogenic fibrosing alveolitis. Am J Respir Crit Care Med 1999, 160:899-905.

23. King TE, Mortenson RL. Cryptogenic organizing pneumonitis. The North American experience. Chest 1992; 102:8S-13S.

24. Moniz D. Pneumonias intersticiais idiopáticas – abordagem diagnóstica. Rev Port Pneumol 2001; VII(4-5):386-92.

25. Ziesche R et al. A preliminary study of long-term treatment with interferon gamma-1b and low-dose prednisolone in patients with idiopathic pulmonary fibrosis. N Engl J Med 1999; 341:1262-9.

26. Raghu G et al. A Placebo-Controlled Trial of Interferon Gamma-1b in Patients with Idiopathic Pulmonary Fibrosis. N Engl J Med 2004; 350:125-33.

27. King TE et al. Analyses of Efficacy End Points in a Controlled Trial of Interferon-ã 1b for Idiopathic Pulmonary Fibrosis. Chest 2005; 127:171-7.

28. International guidelines for the selection of lung transplant candidates. Am J Respir Crit Care Med 1998; 158:335-9.

29. Bjoraker JA et al. Prognostic significance of histopathologic subsets in idiopathic pulmonary fibrosis. Am J Respir Crit Care Med 1998; 157:199-203.

30. Carrington CB et al. Natural history and treated course of usual and desquamative interstitial pneumonia. N Engl J Med 1978; 298:801-9.

 

1Interno (5.º ano) do Internato Complementar de Pneumologia do Hospital de Pulido Valente, Lisboa.

 

Recebido para publicação/received for publication: 05.11.18

Aceite para publicação/accepted for publication: 06.06.20