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Revista Portuguesa de Pneumologia

Print version ISSN 0873-2159

Rev Port Pneumol vol.12 no.4 Lisboa July 2006

 

Hemangioendotelioma epitelióide da pleura: sobrevida de 29 meses

Epithelioid haemangioendothelioma of the pleura: 29 months survival

 

Coordenadora: Lina Carvalho

Anabela Oliveira1

Lina Carvalho2

 

Resumo

O hemangioendotelioma epitelióide da pleura é uma neoplasia rara, com crescimento rápido, de difícil diagnóstico imagiológico e histológico e raramente submetido a tratamento cirúrgico atempado e curativo devido à sobrevida muito curta que condiciona. Em 2005 estavam descritos 31 casos de tumores vasculares na pleura, sendo 11 hemagioendoteliomas epitelióides, aos quais se acrescenta o actual, de uma doente de 52 anos que sofreu um traumatismo toraco-abdominal. Revelou tempo de sobrevida longo (29 meses) após o diagnóstico histológico, ocorrido ocasionalmente por biópsias efectuadas em exame toraco-videoscópico para drenagem de hemotórax. Eram evidentes as lesões vasculares características na pleura direita, sem tradução imagiológica, e houve desenvolvimento de lesão nodular, documentado um mês antes do falecimento da doente.

Palavras-chave: Pleura, hemangioendotelioma epitelióide.

 

 

Abstract

Epithelioid haemangioendothelioma of the pleura is a rare neoplasia with a very poor prognosis due to aggressive involvement of the pleura and incomplete surgical treatment. Histological diagnosis and imagiology is also controversial, related to discrete development of the lesions that later reveal nodules. In 2005 there were 31 cases of vascular tumours described in the pleura. Eleven were epithelioid haemangioendotheliomas. This is another case, a 52 year old woman who suffered a traumatism and died 29 months after the histological diagnosis because CAT revealed discrete pleural involvement and a 2cm nodule was seen only one month before death.

Key-words: Pleura, epithelioid haemangioendothelioma.

 

Texto completo disponível apenas em PDF.

Full text only available in PDF format.

 

 

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1 Assistente Eventual de Medicina Interna do Hospital Distrital de Aveiro

2 Professora de Anatomia Patológica da Faculdade de Medicina de Coimbra

 

Recebido para publicação/received for publication: 06.03.31

Aceite para publicação/accepted for publication: 06.04.22