Abstract

MARINHO, Carla; SILVA, Roberto; COSTA, Fernanda  and  LOPES, José Manuel. Atypical fibrous histiocytoma of the  vulva: report of a rare entity. Acta Obstet Ginecol Port [online]. 2016, vol.10, n.2, pp.148-151. ISSN 1646-5830.

Atypical fibrous histiocytoma is a rare and poorly documented variant of cutaneous fibrous histiocytoma.The vulvar localization is rare. Its clinical behaviour is generally benign; however, it presents histological features associated with malignancy. The pathological differential diagnoses include benign and malignant skin tumors; namely, atypical fibroxanthoma, cutaneous fibrous histiocytoma, cutaneous leiomyosarcoma, malignant fibrous histiocytoma, malignant melanoma, and dermatofibrosarcoma protuberans. We report a new case of atypical vulvar fibrous histiocytoma in a young woman whose diagnosis was based on morphological and immunohistochemical features of the tumor. According our knowledge this is the second documented case of atypical fibrous histiocytoma of the vulva.

Keywords : Atypical fibrous histiocytoma; Vulva.

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