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Revista Portuguesa de Pneumologia

versão impressa ISSN 0873-2159

Resumo

ABREU, Marcus da Matta et al. Primary pleomorphic sarcoma of the lung. Rev Port Pneumol [online]. 2008, vol.14, n.4, pp.535-539. ISSN 0873-2159.

The World Health Organization (WHO) classification of lung cancers ranks the heterogeneous nonsmall cell lung cancer (N-SCLC) group, encompassing sarcoma or sarcoma-containing tumours under one heading: “carcinomas with pleomorphic, sarcomatoid or sarcomatous elements”. This group contains entities such as pleomorphic carcinoma (PC), spindle cell carcinoma (SCC), giant cell carcinoma (GCC), carcinosarcoma (CS) and pulmonary blastoma (PB). These tumors are rare overall, making up approx. 0.1-0.4% of all lung malignancies. They are more commonly found in males who are heavy smokers, diagnosed at the age of 60 on average and follow an aggressive clinical course. The authors describe the case of a male patient with primary pleomorphic lung sarcoma and also include a review of the literature.

Palavras-chave : Lung neoplasms; pleomorphic sarcoma; conective and soft tissue neoplasms.

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