Resumo

COUTO, Gilberto et al. Small duct primary sclerosing cholangitis. J Port Gastrenterol. [online]. 2012, vol.19, n.4, pp.204-208. ISSN 0872-8178.

We report the clinical case of an 18-year-old woman admitted with Crohn’s disease with colitis and gastro duodenal involvement, anasarca, pyoderma gangrenosum and a pattern of anicteric cholestasis. The MR-cholangiogram was normal and liver biopsy suggested the presence of primary sclerosing cholangitis, thus making the diagnosis of small duct primary sclerosing cholangitis. We review the state-of-the-art on this very rare disease, which seems a different clinical entity than large duct primary sclerosing cholangitis, and with a better prognosis.

Palavras-chave : Primary sclerosing cholangitis; Small duct primary sclerosing cholangitis; Crohn’s disease.

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