Abstract

MARTINS, João Rio; NEVES, João Fonseca; SILVA, Teresa Reis  and  FELIX, Miguel. Chronic rhinosinusitis with bone destruction in a teenager with cystic fibrosis. Nascer e Crescer [online]. 2019, vol.28, n.2, pp.87-89. ISSN 0872-0754.  https://doi.org/10.25753/BirthGrowthMJ.v28.i2.14853.

Introduction: Chronic rhinosinusitis (CRS) is almost invariably present in cystic fibrosis (CF) patients, with a detrimental impact in their quality of life. Functional endoscopic sinus surgery (FESS) has been proven effective when medical management approaches are exhausted. Case Summary: A twelve-year-old female with CF and a several-month history of intermittent fever, recurrent cough, and purulent sputum despite intensive medical management was admitted due to fever and frontal headaches starting a few days after initiation of nocturnal non-invasive ventilation. Perinasal and cerebral sinuses' computed tomography scan and magnetic resonance imaging showed a severe CRS complicated with bone destruction of the left frontal sinus and crista galli. Intravenous antibiotics and antifungal were started, and FESS was performed with significant clinical improvement. Microbiologic study was positive for methicillin-resistant Staphylococcus aureus. Discussion: This case shows that regular assessment of sinusal disease in CF children is essential, especially in those with chronic infections. FESS may be usefull when medical management approaches are exhausted, effectively improving patients's quality of life.

Keywords : bone destruction; chronic rhinosinusitis; cystic fibrosis; endoscopic sinus surgery; methicillin-resistant Staphylococcus aureus.

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